VI. DISEASES OF THE NERVOUS SYSTEM AND SENSE ORGANS INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326) 320 Bacterial meningitis Includes: arachnoiditis bacterial leptomeningitis bacterial meningitis bacterial meningoencephalitis bacterial meningomyelitis bacterial pachymeningitis bacterial 320.0 Hemophilus meningitis Meningitis due to Hemophilus influenzae [H. influenzae] 320.1 Pneumococcal meningitis 320.2 Streptococcal meningitis 320.3 Staphylococcal meningitis 320.8 Meningitis due to other specified bacteria Meningitis due to: escherichia coli [E. coli] Friedl„nder bacillus 320.9 Meningitis due to unspecified bacterium Meningitis: bacterial NOS purulent NOS pyogenic NOS suppurative NOS 322 Meningitis of unspecified cause Includes: arachnoiditis with no organism specified as cause leptomeningitis with no organism specified as cause meningitis with no organism specified as cause pachymeningitis with no organism specified as cause 322.0 Nonpyogenic meningitis Meningitis with clear cerebrospinal fluid 322.1 Eosinophilic meningitis 322.2 Chronic meningitis 322.9 Meningitis, unspecified ICD-9/Ch06.TXT - pg. 1 323 Encephalitis, myelitis, and encephalomyelitis Includes: acute disseminated encephalomyelitis meningoencephalitis, except bacterial meningomyelitis, except bacterial myelitis (acute): ascending transverse Excludes: bacterial: meningoencephalitis meningomyelitis 323.5 Encephalitis following immunization procedures Encephalitis postimmunization or postvaccinal Encephalomyelitis postimmunization or postvaccinal Use additional E code, if desired, to identify vaccine 323.8 Other 323.9 Unspecified cause 324 Intracranial and intraspinal abscess 324.0 Intracranial abscess Abscess (embolic) of brain Abscess (embolic): [any part]: cerebellar epidural cerebral extradural otogenic subdural 324.1 Intraspinal abscess Abscess (embolic) of spinal cord [any part]: epidural extradural subdural 324.9 Of unspecified site Extradural or subdural abscess NOS 325 Phlebitis and thrombophlebitis of intracranial venous sinuses Embolism } Endophlebitis } of cavernous, lateral, or other Phlebitis, septic or suppurative } intracranial or unspecified Thrombophlebitis } intracranial venous sinus Thrombosis } ICD-9/Ch06.TXT - pg. 2 Excludes: when specified as: complicating pregnancy, childbirth, or the puerperium (671.5) of nonpyogenic origin (437.6) 326 Late effects of intracranial abscess or pyogenic infection Note: This category is to be used to indicate conditions whose primary classification is to 320-325 as the cause of late effects, themselves classifiable elsewhere. The "late effects" include conditions specified as such, or as sequelae, which may occur at any time after the resolution of the causal condition. HEREDITARY AND DEGENERATIVE DISEASES OF THE CENTRAL NERVOUS SYSTEM (330-337) Excludes: hepatolenticular degeneration (275.1) multiple sclerosis (340) other demyelinating diseases of central nervous system (341.-) 330 Cerebral degenerations usually manifest in childhood Use additional code, if desired, to identify associated mental retardation 330.0 Leukodystrophy Krabbe's disease Leukodystrophy: NOS globoid cell metachromatic sudanophilic 330.1 Cerebral lipidoses Amaurotic (family) idiocy Disease: Batten Jansky-Bielschowsky Kufs Spielmeyer-Vogt Tay-Sachs Gangliosidosis 330.8 Other cerebral degenerations in childhood Alpers' disease or gray-matter degeneration Leigh's disease or subacute necrotizing encephalopathy 330.9 Unspecified ICD-9/Ch06.TXT - pg. 3 331 Other cerebral degenerations Use additional code, if desired, to identify associated mental disorder 331.0 Alzheimer's disease 331.1 Pick's disease 331.2 Senile degeneration of brain Excludes: senility NOS (797) 331.3 Communicating hydrocephalus Excludes: congenital hydrocephalus (741.0, 742.3) 331.4 Obstructive hydrocephalus Acquired hydrocephalus NOS Excludes: congenital hydrocephalus (741.0, 742.3) 331.8 Other cerebral degeneration 331.9 Unspecified 332 Parkinson's disease 332.0 Paralysis agitans Parkinsonism or Parkinson's disease: NOS idiopathic primary 332.1 Secondary Parkinsonism Parkinsonism: due to drugs Use additional E code, if desired, to identify drug, if drug-induced 333 Other extrapyramidal disease and abnormal movement disorders Includes: other forms of extrapyramidal, basal ganglia, or striatopallidal disease Excludes: abnormal movements of head NOS (781.0) 333.0 Other degenerative diseases of the basal ganglia Atrophy or degeneration: ICD-9/Ch06.TXT - pg. 4 Hallervorden-Spatz disease or pigmentary pallidal degeneration Olivopontocerebellar degeneration Parkinsonian syndrome associated with: idiopathic orthostatic hypotension symptomatic orthostatic hypotension Progressive supranuclear ophthalmoplegia Shy-Drager syndrome Striatonigral degeneration 333.1 Essential and other specified forms of tremor Benign essential tremor Familial tremor Use additional E code, if desired, to identify drug, if drug-induced Excludes: tremor NOS (781.0) 333.2 Myoclonus Familial essential myoclonus Unverricht-Lundborg disease Progressive myoclonic epilepsy Use additional E code, if desired, to identify drug, if drug-induced 333.3 Tics of organic origin Excludes: Gilles de la Tourette's syndrome (307.2) habit spasm (307.2) tic NOS (307.2) Use additional E code, if desired, to identify drug, if drug-induced 333.4 Huntington's chorea 333.5 Other choreas Hemiballism(us) Paroxysmal choreo-athetosis Excludes: Sydenham's or rheumatic chorea (392.-) Use additional E code, if desired, to identify drug, if drug-induced 333.6 Idiopathic torsion dystonia Dystonia musculorum deformans or (Schwalbe-) Ziehen-Oppenheim disease 333.7 Symptomatic torsion dystonia Athetoid cerebral palsy or Vogt's disease Double athetosis Use additional E code, if desired, to identify drug, if drug-induced ICD-9/Ch06.TXT - pg. 5 333.8 Fragments of torsion dystonia Blepharospasem Orofacial duskinesia Organic writer' cramp Spasmodic torticollis Use additional E code, if desired, to identify drug, if drug-induced 333.9 Other and unspecified Restless legs Stiff man syndrome 334 Spinocerebellar disease Excludes: olivopontocerebellar degeneration (333.0) peroneal muscular atrophy (356.1) 334.0 Friedreich's ataxia 334.1 Hereditary spastic paraplegia 334.2 Primary cerebellar degeneration Primary cerebellar degeneration: NOS hereditary sporadic 334.3 Other cerebellar ataxia Cerebellar ataxia NOS Use additional E code to identify drug, if drug-induced 334.8 Other Ataxia-telangiectasia or Louis-Bar syndrome 334.9 Unspecified 335 Anterior horn cell disease 335.0 Werdnig-Hoffmann disease Infantile spinal muscular atrophy 335.1 Spinal muscular atrophy Kugelberg-Welander disease Adult spinal muscular atrophy 335.2 Motor neuron disease Amyotrophic lateral sclerosis Progressive muscular atrophy (pure) Motor neuron disease (bulbar) (mixed type) ICD-9/Ch06.TXT - pg. 6 335.8 Other 335.9 Unspecified 336 Other diseases of spinal cord 336.0 Syringomyelia and syringobulbia 336.1 Vascular myelopathies Acute infarction of spinal cord (embolic) (nonembolic) Arterial thrombosis of spinal cord Edema of spinal cord Hematomyelia Subacute necrotic myelopathy 336.8 Other myelopathy Myelopathy: drug-induced radiation-induced Use additional E code, if desired, to identify cause 336.9 Unspecified diseases of spinal cord Cord compression NOS Myelopathy NOS Excludes: myelitis (323.-) 337 Disorders of the autonomic nervous system Includes: disorders of peripheral autonomic, sympathetic, parasym-pathetic, or vegetative system Excludes: familial dysautonomia [Riley-Day syndrome] (742.8) 337.0 Idiopathic peripheral autonomic neuropathy 337.9 Unspecified OTHER DISORDERS OF THE CENTRAL NERVOUS SYSTEM (340-349) 340 Multiple sclerosis Disseminated or multiple sclerosis: NOS brain stem cord generalized ICD-9/Ch06.TXT - pg. 7 341 Other demyelinating diseases of central nervous system 341.0 Neuromyelitis optica 341.1 Schilder's disease Balo's concentric sclerosis Encephalitis periaxialis: concentrica diffusa 341.8 Other 341.9 Unspecified 342 Hemiplegia Note: For primary coding, this category is to be used only when hemiplegia (complete) (incomplete), except of types listed in 343.1 and 343.4, is reported without further specification, or is stated to be old or long-standing but of unspecified cause. The category is also for use in multiple coding to identify these types of hemiplegia resulting from any cause. 342.0 Flaccid hemiplegia 342.1 Spastic hemiplegia 342.9 Unspecified 343 Infantile cerebral palsy Includes: cerebral: palsy NOS spastic infantile paralysis congenital spastic paralysis (cerebral) Little's disease paralysis (spastic) due to birth injury: intracranial spinal Excludes: hereditary cerebral paralysis, such as: hereditary spastic paraplegia (334.1) Vogt's disease (333.7) 343.0 Diplegic Congenital diplegia Congenital paraplegia 343.1 Hemiplegic Congenital hemiplegia Excludes: infantile hemiplegia NOS (343.4) ICD-9/Ch06.TXT - pg. 8 343.2 Quadriplegic Tetraplegic 343.3 Monoplegic 343.4 Infantile hemiplegia Infantile hemiplegia (postnatal) NOS 343.8 Other 343.9 Unspecified 344 Other paralytic syndromes Note: For primary coding, this category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause. Includes: paralysis (complete) (incomplete), except as in 342.- and 343.- 344.0 Quadriplegia 344.1 Paraplegia Paralysis of both lower limbs Paraplegia (lower) 344.2 Diplegia of upper limbs Diplegia (upper) Paralysis of both upper limbs 344.3 Monoplegia of lower limb Paralysis of lower limb 344.4 Monoplegia of upper limb Paralysis of upper limb 344.5 Unspecified monoplegia 344.6 Cauda equina syndrome Cord bladder Neurogenic bladder 344.8 Other 344.9 Unspecified ICD-9/Ch06.TXT - pg. 9 345 Epilepsy Excludes: progressive myoclonic epilepsy (333.2) 345.0 Generalized nonconvulsive epilepsy Absences: Seizures: atonic akinetic typical atonic Petit mal 345.1 Generalized convulsive epilepsy Epileptic seizures: Grand mal clonic Major epilepsy myoclonic tonic tonic-clonic Excludes: infantile spasms (345.6) 345.2 Petit mal status Epileptic absence status 345.3 Grand mal status Status epilepticus NOS Excludes: epilepsia partialis continua (345.7) 345.4 Partial epilepsy, with impairment of consciousness Epilepsy: Epileptic automatism partial: secondarily generalized with memory and ideational disturbances psychomotor psychosensory 345.5 Partial epilepsy, without mention of impairment of consciousness Epilepsy: Epilepsy: Bravais-Jacksonian NOS somatomotor focal (motor) NOS somatosensory Jacksonian NOS visceral motor partial visual partial NOS 345.6 Infantile spasms Hypsarrhythmia Salaam attacks Lightning spasms ICD-9/Ch06.TXT - pg. 10 Excludes: salaam tic (781.0) 345.7 Epilepsia partialis continua Kojevnikov's epilepsy 345.8 Other 345.9 Unspecified Epileptic convulsions, fits, or seizures NOS 346 Migraine 346.0 Classical migraine Migraine preceded or accompanied by transient focal neurological phenomena Migraine with aura 346.1 Common migraine 346.2 Variants of migraine Cluster headache Neuralgia: Migraine: ciliary basilar migrainous lower half retinal 346.8 Other Migraine: hemiplegic ophthalmoplegic 346.9 Unspecified 347 Cataplexy and narcolepsy 348 Other conditions of brain 348.0 Cerebral cysts Arachnoid cyst Porencephalic cyst 348.1 Anoxic brain damage Excludes: when attributable to medical care for abortion, ectopic or molar pregnancy, labor or delivery (634-638) with fourth digit .7, 639.8, 668.2, 669.4) when of newborn (767.0, 768.-, 772.1-772.2) Use additional E code, if desired, to identify cause [e.g., anaesthesia] ICD-9/Ch06.TXT - pg. 11 348.2 Benign intracranial hypertension 348.3 Encephalopathy, unspecified 348.4 Compression of brain Compression brain (stem) Herniation brain (stem) 348.5 Cerebral edema 348.8 Other Cerebral: calcification fungus 348.9 Unspecified 349 Other and unspecified disorders of the nervous system 349.0 Reaction to spinal or lumbar puncture Headache following lumbar puncture 349.1 Nervous system complications from surgically implanted device Excludes: immediate postoperative complications (997.0) mechanical complications classifiable to 996.2 (996.2) 349.2 Disorders of meninges, not elsewhere classified Adhesions, meningeal (cerebral) (spinal) 349.8 Other 349.9 Unspecified DISORDERS OF THE PERIPHERAL NERVOUS SYSTEM (350-359) Excludes: diseases of: acoustic [8th] nerve (388.5) oculomotor [3rd, 4th, 6th] nerves (378.-) optic [2nd] nerve (377.-) neuralgia NOS or "rheumatic" (729.2) neuritis NOS or "rheumatic" (729.2) radiculitis NOS or "rheumatic" (729.2) peripheral neuritis in pregnancy (646.4) 350 Trigeminal nerve disorders Includes: disorders of 5th cranial nerve ICD-9/Ch06.TXT - pg. 12 350.1 Other trigeminal neuralgia 350.2 Atypical face pain 350.8 Other 350.9 Unspecified 351 Facial nerve disorders Includes: disorders of 7th cranial nerve 351.0 Bell's palsy Facial palsy 351.1 Geniculate ganglionitis Geniculate ganglionitis: NOS 351.8 Other 351.9 Unspecified 352 Disorders of other cranial nerves 352.0 Disorders of olfactory [1st] nerve 352.1 Glossopharyngeal neuralgia 352.2 Other disorders of glossopharyngeal [9th] nerve 352.3 Disorders of pneumogastric [10th] nerve 352.4 Disorders of accessory [11th] nerve 352.5 Disorders of hypoglossal [12th] nerve 352.6 Multiple cranial nerve palsies Polyneuritis cranialis 352.9 Unspecified 353 Nerve root and plexus disorders Excludes: conditions due to: intervertebral disc disorders (722.-) spondylosis (720.-, 721.-) vertebrogenic disorders (723.-, 724.-) ICD-9/Ch06.TXT - pg. 13 353.0 Brachial plexus lesions Excludes: brachial neuritis or radiculitis NOS (723.4) 353.1 Lumbosacral plexus lesions 353.2 Cervical root lesions, not elsewhere classified 353.3 Thoracic root lesions, not elsewhere classified 353.4 Lumbosacral root lesions, not elsewhere classified 353.5 Neuralgic amyotrophy Parsonage-Aldren-Turner syndrome 353.6 Phantom limb 353.8 Other 353.9 Unspecified 354 Mononeuritis of upper limb and mononeuritis multiplex 354.0 Carpal tunnel syndrome 354.1 Other lesion of median nerve 354.2 Lesion of ulnar nerve Tardy ulnar nerve palsy 354.3 Lesion of radial nerve 354.4 Causalgia 354.5 Mononeuritis multiplex Combinations of single conditions classifiable to 354.- or to 355.- 354.8 Other 354.9 Unspecified 355 Mononeuritis of lower limb 355.0 Lesion of sciatic nerve Excludes: sciatica NOS (724.3) 355.1 Meralgia paresthetica Lateral cutaneous nerve of thigh syndrome ICD-9/Ch06.TXT - pg. 14 355.2 Lesion of femoral nerve 355.3 Lesion of lateral popliteal nerve 355.4 Lesion of medial popliteal nerve 355.5 Tarsal tunnel syndrome 355.6 Lesion of plantar nerve Morton's metatarsalgis 355.7 Other 355.8 Unspecified Mononeuritis of lower limb 355.9 Mononeuritis of unspecified site 356 Hereditary and idiopathic peripheral neuropathy 356.0 Hereditary peripheral neuropathy Dejerine-Sottas disease 356.1 Peroneal muscular atrophy Charcot-Marie-Tooth disease 356.2 Hereditary sensory neuropathy 356.3 Refsum's disease 356.4 Idiopathic progressive polyneuropathy 356.8 Other specified idiopathic peripheral neuropathy 356.9 Unspecified 357 Inflammatory and toxic neuropathy 357.0 Acute infective polyneuritis Guillain-Barre syndrome 357.5 Alcoholic polyneuropathy 357.6 Polyneuropathy due to drugs Use additional E code, if desired, to identify drug ICD-9/Ch06.TXT - pg. 15 357.7 Polyneuropathy due to other toxic agents Use additional E code, if desired, to identify toxic agent 357.8 Other 357.9 Unspecified 358 Myoneural disorders 358.0 Myasthenia gravis 358.2 Toxic myoneural disorders Use additional E code, if desired, to identify toxic agent 358.8 Other 358.9 Unspecified 359 Muscular dystrophies and other myopathies Excludes: idiopathic polymyositis (710.4) 359.0 Congenital hereditary muscular dystrophy Benign congenital myopathy Myotubular myopathy Central core disease Nemaline body disease Excludes: arthrogryposis multiplex congenita (755.8) 359.1 Hereditary progressive muscular dystrophy Muscular dystrophy: Muscular dystrophy: NOS Landouzy-Dejerine distal limb-girdle Duchenne ocular Erb's oculopharyngeal fascioscapulohumeral 359.2 Myotonic disorders Dystrophia myotonica Paramyotonia congenita Myotonia congenita Steinert's disease 359.3 Familial periodic paralysis Hypokalemic familial periodic paralysis 359.4 Toxic myopathy Use additional E code, if desired, to identify toxic agent ICD-9/Ch06.TXT - pg. 16 359.8 Other 359.9 Unspecified DISORDERS OF THE EYE AND ADNEXA (360-379) 360 Disorders of the globe Includes: disorders affecting multiple structures of eye 360.0 Purulent endophthalmitis Panophthalmitis Vitreous abscess 360.1 Other endophthalmitis Ophthalmia nodosa Sympathetic uveitis Parasitic endophthalmitis NOS 360.2 Degenerative disorders of globe Chalcosis Siderosis of eye Malignant myopia 360.3 Hypotony of eye 360.4 Degenerated conditions of globe Absolute glaucoma Haemophthalmos Atrophy of globe Phthisis bulbi 360.5 Retained (old) intraocular foreign body, magnetic Retained (old) magnetic foreign body (in): anterior chamber ciliary body iris lens vitreous posterior wall 360.6 Retained (old) intraocular foreign body, nonmagnetic Retained (old) foreign body in sites listed in 360.5: NOS nonmagnetic 360.8 Other disorders of globe Luxation of globe 360.9 Unspecified ICD-9/Ch06.TXT - pg. 17 361 Retinal detachments and defects 361.0 Retinal detachment with retinal defect Giant tear of retina (with detachment) Rhegmatogenous retinal detachment 361.1 Retinoschisis and retinal cysts Cyst of ora serrata Pseudocust of retina Excludes: microcystoid degeneration of retina (362.6) parasitic cyst of retina (360.1) 361.2 Serous retinal detachment Retinal detachment without retinal defect 361.3 Retinal defects without detachment Horseshoe tear } Round hole } of retina, without mention of detachment Operculum } 361.8 Other forms of retinal detachment Traction detachment of retina 361.9 Unspecified 362 Other retinal disorders Excludes: chorioretinal scars (363.3) chorioretinitis (363.-) 362.1 Other background retinopathy and retinal vascular changes Changes in retinal vascular Retinopathy: appearance NOS Retinal: atherosclerotic(440.8) micro-arneurysms NOS background NOS neovascularization NOS Coat's perivasculits exudative varices vascular sheathing vasculitis 362.2 Other proliferative retinopathy Retrolental fibroplasia 362.3 Retinal vascular occlusion ICD-9/Ch06.TXT - pg. 18 Microembolism, retinal Occlusion (partial) (total) (transient): retinal artery (branch) (central) retinal vein (central) (tributary) Venous engorgement, retina 362.4 Separation of retinal layers Central serous chorioretinopathy Detachment of retinal pigment epithelium Excludes: serous retinal detachment (361.2) 362.5 Degeneration of macula and posterior pole Cyst } Kuhnt-Junius degeneration Hole } of macula Senile macular generation Puckering } (atrophic)(exudative) Drusen (degenerative) Toxic maculopathy Use additional E code, if desired, to identify drug, if drug-induced 362.6 Peripheral retinal degenerations Degeneration, retina: Degeneration, retina: lattice paving stone microcystoid peripheral palisade reticular 362.7 Hereditary retinal dystrophies Dystrophy: Retinitis pigmentosa retinal (albipunctate) Stargardt's disease (pigmentary) (vitelliform) tapetoretinal vitreoretinal 362.8 Other retinal disorders Hemorrhage: Retinal: preretinal cotton wool spots retinal (deep) edema (localized) (macular) (peripheral) (superficial) exudes subretinal ischemia Excludes: chorioretinal inflammations and scars (363.-) 362.9 Unspecified 363 Chorioretinal inflammations, scars, and other disorders of choroid ICD-9/Ch06.TXT - pg. 19 363.0 Focal chorioretinitis and focal retinochoroiditis Focal: chorioretinitis or choroiditis retinochoroiditis or retinitis: NOS 363.1 Disseminated chorioretinitis and disseminated retinochoroiditis Disseminated: choroiditis or chorioretinitis NOS retinitis or retinochoroiditis NOS Excludes: retinal: perivasculitis (362.1) vasculitis (362.1) 363.2 Other and unspecified forms of chorioretinitis and retinochoroiditis Pars planitis Posterior cyclitis Excludes: panophthalmitis (360.02) sympathetic uveitis (360.11) 363.3 Chorioretinal scars Scar (postinflammatory) (postsurgical) (posttraumatic): choroid macula posterior pole retina Solar retinopathy 363.4 Choroidal degenerations Angioid streaks of choroid Atropy of choroid Sclerosis of choriod 363.5 Hereditary choroidal dystrophies Choroideremia Dystrophy, choroidal (central areolar) (generalized) (gyrate) (peripapillary) Gyrate atrophy, choroid 363.6 Choroidal hemorrhage and rupture Choroidal hemorrhage: NOS expulsive ICD-9/Ch06.TXT - pg. 20 363.7 Choroidal detachment 363.8 Other disorders of choroid 363.9 Unspecified 364 Disorders of iris and ciliary body 364.0 Acute and subacute iridocyclitis Anterior uveitis } acute Cyclitis } recurrent Iridocyclitis } subacute Iritis } with hypopyon 364.1 Chronic iridocyclitis Iridocyclitis: chronic 364.2 Certain types of iridocyclitis Fuchs's heterochromic cyclitis Lens-induced iridocyclitis Glaucomatocyclitic crises 364.3 Unspecified iridocyclitis 364.4 Vascular disorders of iris and ciliary body Hemorrhage of iris or ciliary body Neovascularization of iris or ciliary body Hyphaema Rubeosis of iris 364.5 Degenerations of iris and ciliary body Degeneration: Miotic pupillary cyst iris (pigmentary) Translucency of iris pupillary margin Iris atrophy (essential) (progressive) Iridoschisis 364.6 Cysts of iris, ciliary body, and anterior chamber Cyst of iris, ciliary body or anterior chamber: NOS exudative implantation Excludes: miotic pupillary cyst (364.5) parasitic cyst (360.1) 364.7 Adhesions and disruptions of iris and ciliary body ICD-9/Ch06.TXT - pg. 21 Ectopic pupil Recession, chamber angle Goniosynechias Synechiae (iris): Iridodialysis NOS Pupillary: anterior membranes posterior occlusion seclusion 364.8 Other disorders of iris and ciliary body 364.9 Unspecified 365 Glaucoma Excludes: glaucoma: absolute (360.4) congenital (743.2) 365.0 Borderline glaucoma Anatomical narrow angle Open-angle with: Ocular hypertension borderline intraocular presssure Steoid responder cupping of discs 365.1 Open-angle glaucoma Glaucoma (primary) (residual stage): chronic simple low tension open angle pigmentary 365.2 Primary angle-closure glaucoma Angle-closure glaucoma (primary) (residual stage): acute chronic intermittent 365.3 Corticosteroid-induced glaucoma Corticosteroid-induced glaucoma (glaucomatous stage) (residual stage) Use additional E code, if desired, to identify drug 365.4 Glaucoma associated with congenital anomalies, with dystrophies, and with systemic syndromes 365.5 Glaucoma associated with disorders of the lens Glaucoma (in): Glaucoma (in): hypermature cataract pseudoexfoliation of capsule postdislocation of lens phacolytic glaucoma ICD-9/Ch06.TXT - pg. 22 365.6 Glaucoma associated with other ocular disorders Glaucoma in: Glaucoma (in): concussion of globe rubeosis of iris iridocyclitis tumours of globe retinal vein occlusion 365.8 Other glaucoma Hypersecretion glaucoma 365.9 Unspecified 366 Cataract Excludes: congenital cataract (743.3) 366.0 Infantile, juvenile, and presenile cataract 366.1 Senile cataract Senile cataract (hypermature) (incipient) (mature) Pseudoexfoliation of (lens) capsule 366.2 Traumatic cataract 366.3 Cataract secondary to ocular disorders Cataracta complicata Cataract in chronic iridocyclitis Glaucomatous flecks (subcapsular) 366.4 Cataract associated with other disorders Cataract: drug-induced Use additional E code, if desired, to identify cause if due to drug or other toxic substance 366.5 After-cataract Secondary cataract Soemering's ring 366.8 Other cataract 366.9 Unspecified 367 Disorders of refraction and accommodation 367.0 Hypermetropia ICD-9/Ch06.TXT - pg. 23 367.1 Myopia 367.2 Astigmatism 367.3 Anisometropia and aniseikonia 367.4 Presbyopia 367.5 Disorders of accommodation Internal ophthalmoplegis Paresis of accommodation (complete) (total) Spasm of accommodation 367.8 Other 367.9 Unspecified 368 Visual disturbances Excludes: electrophysiological disturbances (794.1) 368.0 Amblyopia ex anopsia Amblyopia: Amblyopia: deprivation suppression strabismic 368.1 Subjective visual disturbances Asthenopia Sudden visual loss Metamorphopsia Visual: Photophobia hallucinations Scintillating scotoma halos 368.2 Diplopia Double vision 368.3 Other disorders of binocular vision Abnormal retinal correspondence Fusion with defective stereopsis Simultaneous visual perception without fusion Suppression of binocular vision 368.4 Visual field defects Enlarged blind spot Scotoma: Generalized contraction of arcuate visual field Bjerrum Hemianop(s)ia (heteronymous) central (homonymous) ring Quadrant anop(s)ia ICD-9/Ch06.TXT - pg. 24 368.5 Color vision deficiencies Achromatopsia Protanopia Deuteranomaly Tritanomaly Deuteranopia Tritanopia Protanomaly 368.6 Night blindness Night blindness: NOS 368.8 Other visual disturbances 368.9 Unspecified 369 Blindness and low vision 369.0 Blindness, both eyes 369.1 Blindness, one eye, low vision other eye 369.2 Low vision, both eyes 369.3 Unqualified visual loss, both eyes 369.6 Blindness, one eye 369.7 Low vision, one eye 369.8 Unqualified visual loss, one eye 369.9 Unspecified visual loss Note: The table below gives a classification of severity of visual impairment recommended by a WHO Study Group on the Prevention of Blindness, Geneva, 6-10 November 1972.1 The term "low vision" in the above category comprises categories 1 and 2 of the table below, the term "blindness" categories 3, 4 and 5 and the term "unqualified visual loss" category 9. 370 Keratitis 370.0 Corneal ulcer Ulcer: cornea (central) (marginal) (perforated) (ring) hypopyon Mooren's ICD-9/Ch06.TXT - pg. 25 ____________________________________________________________________________ Category of | Visual acuity with best possible correction visual |________________________________________________________________ impairment | maximum less than | minimum equal to or better than ____________|______________________________|_________________________________ | | | 6/18 | 6/60 1 | 3/10 (0.3) | 1/10 (0.1) | 20/70 | 20/200 ____________|______________________________|_________________________________ | | | 6/60 | 3/60 2 | 1/10 (0.1) | 1/20 (0.05) | 20/200 | 20/400 ____________|______________________________|_________________________________ | | | 3/60 | 1/60 (finger counting at 3 | | 1 metre) | 1/20 (0.05) | 1/50 (0.02) | 20/400 | 5/300 (20/1200) ____________|______________________________|_________________________________ | | | 1/60 (finger counting at | 4 | 1 metre) | Light perception | 1/50 (0.02) | | 5/300 (20/1200) | ____________|______________________________|_________________________________ | 5 | No light perception ____________|________________________________________________________________ | 9 | Undetermined or unspecified ____________|________________________________________________________________ If the extent of the visual field is taken into account, patients with a field no greater than 10ø but greater than 5ø around central fixation should be placed in category 3 and patients with a field no greater than 5ø around central fixation should be placed in category 4, even if the central acuity is not impaired. 370.2 Other superficial keratitis without conjunctivitis Keratitis: Keratitis: areolar striate filamentary superficial punctate nummular Photokeratitis stellate Snow blindness ICD-9/Ch06.TXT - pg. 26 370.3 Certain types of keratoconjunctivitis Keratoconjunctivitis: exposure neurotrophic phlyctenular 370.4 Other and unspecified keratoconjunctivitis Keratitis or keratoconjunctivitis in other exanthemata NOS Superficial keratitis with conjunctivitis 370.5 Interstitial and deep keratitis Corneal abscess Keratitis: Interstitial keratitis: sclerosing NOS nonsyphilitic 370.6 Corneal neovascularization Ghost vessels (corneal) Pannus (corneal) 370.8 Other forms of keratitis 370.9 Unspecified 371 Corneal opacity and other disorders of cornea 371.0 Corneal scars and opacities Corneal: leucoma (adherent)) macula nebula 371.1 Corneal pigmentations and deposits Haematocornea Krukenberg spindle Kayser-Fleischer ring Staehli's line 371.2 Corneal edema Bullous keratopathy 371.3 Changes of corneal membranes Fold in Descemet's membrane Rupture in Descemet's membrane ICD-9/Ch06.TXT - pg. 27 371.4 Corneal degenerations Arcus senilis Recurrent corneal erosion Band-shaped keratopathy Excludes: Mooren's ulcer (370.0) 371.5 Hereditary corneal dystrophies Corneal dystrophy (epithelial) (granular) (lattice) (macular) Fuchs's endothelial dystrophy 371.6 Keratoconus 371.7 Other corneal deformities Corneal ectasia Descemetocele Corneal staphyloma 371.8 Other corneal disorders Anesthesia } of Hypoesthesia } cornea 371.9 Unspecified 372 Disorders of conjunctiva Excludes: keratoconjunctivitis (370.3, 370.4) 372.0 Acute conjunctivitis Conjunctivitis: mucopurulent serous Excludes: ophthalmia neonatorum NOS 372.1 Chronic conjunctivitis Vernal conjunctivitis 372.2 Blepharoconjunctivitis 372.3 Other and unspecified conjunctivitis 372.4 Pterygium Excludes: pseudopterygium (372.5) 372.5 Conjunctival degenerations and deposits ICD-9/Ch06.TXT - pg. 28 Conjunctival: Conjunctival xerosis: argyrosis NOS concretions Pseudopterygium pigmentation 372.6 Conjunctival scars Symblepharon 372.7 Conjunctival vascular disorders and cysts Aneurysm of conjunctiva Hyposphagma Chemosis of conjunctiva Subconjunctival haemorrhage 372.8 Other disorders of conjunctiva 372.9 Unspecified 373 Inflammation of eyelids 373.0 Blepharitis Excludes: blepharoconjunctivitis (372.2) 373.1 Hordeolum and other deep inflammation of eyelid Abscess of eyelid Stye Furuncle of eyelid 373.2 Chalazion Meibomian (gland) cyst 373.3 Noninfectious dermatoses of eyelid Dermatitis: } allergic } contact } of eyelid exzematous } Discoid lupus erythematosus } Xeroderma } 373.8 Other 373.9 Unspecified 374 Other disorders of eyelids 374.0 Entropion and trichiasis of eyelid 374.1 Ectropion 374.2 Lagophthalmos ICD-9/Ch06.TXT - pg. 29 374.3 Ptosis of eyelid Blepharochalasis 374.4 Other disorders affecting eyelid function Ankyloblepharon Lid retraction Blepharophimosis Excludes: blepharospasm (333.8) tic (psychogenic) (307.2) organic (333.3) 374.5 Degenerative disorders of eyelid and periocular area Chloasma } Hypertrichosis } of eyelid Vitiligo } Madarosis 374.8 Other disorders of eyelid Retained foreign body in eyelid 374.9 Unspecified 375 Disorders of lacrimal system 375.0 Dacryoadenitis Chronic enlargement of lacrimal gland 375.1 Other disorders of lacrimal gland Dacryops Lacrimal: Dry eye syndrome atrophy cyst 375.2 Epiphora 375.3 Acute and unspecified inflammation of lacrimal passages Canaliculitis, lacrimal } NOS Dacryocystitis (phlegmonous) } acute Dacryopericystitis } subacute Excludes: neonatal dacryocystitis (771.6) 375.4 Chronic inflammation of lacrimal passages Canaliculitis, lacrimal } Dacryocystitis (phlegmonous) } chronic Mucocele, lacrimal } ICD-9/Ch06.TXT - pg. 30 375.5 Stenosis and insufficiency of lacrimal passages Dacryolith Eversion of lacrimal punctum Stenosis: lacrimal canaliculi punctum sac nasolacrimal duct 375.6 Other changes of lacrimal passages Lacrimal fistula 375.8 Other disorders of lacrimal system 375.9 Unspecified 376 Disorders of the orbit 376.0 Acute inflammation of orbit Cellulitis } Tenonitis Abscess } of orbit periostitis } Osteomyelitis } 376.1 Chronic inflammatory disorders of orbit Granuloma } Pseudotumor } of orbit Myositis } 376.3 Other exophthalmic conditions Displacement of globe Hemorrhage } of orbit (lateral) NOS Edema } Exophthalmos 376.4 Deformity of orbit Atrophy of orbit Exostosis of orbit 376.5 Enophthalmos 376.6 Retained (old) foreign body following penetrating wound of orbit Retrobulbar foreign body 376.8 Other disorders of orbit Cyst of orbit Myopathy of extraocular muscles ICD-9/Ch06.TXT - pg. 31 376.9 Unspecified 377 Disorders of optic nerve and visual pathways 377.0 Papilledema 377.1 Optic atrophy Optic atrophy: NOS Temporal pallor, optic disc 377.2 Other disorders of optic disc Drusen of optic disc Pseudopapilledema Coloboma of optic disc 377.3 Optic neuritis Optic neuropathy, except Retrobulbar neuritis: ischemic NOS Optic papillitis 377.4 Other disorders of optic nerve Compression of optic nerve Hemorrhage in optic nerve sheath Optic neuropathy, ischaemic 377.5 Disorders of optic chiasm 377.6 Disorders of other visual pathways Disorders of optic tracts, geniculate nuclei and optic radiations 377.7 Disorders of visual cortex 377.9 Unspecified 378 Strabismus and other disorders of binocular eye movements Excludes: nystagmus and other irregular eye movements (379.5) 378.0 Convergent concomitant strabismus Esotropia (alternating) (monocular), except intermittent 378.1 Divergent concomitant strabismus Exotropia (alternating) (monocular), except intermittent ICD-9/Ch06.TXT - pg. 32 378.2 Intermittent heterotropia Intermittent: esotropia } (alternating) exotropia } (monocular) 378.3 Other and unspecified heterotropia Hypertropia Microtropia Vertical heterotropia Monofixation syndrome Hypotropia Concomitant strabismus NOS Cyclotropia 378.4 Heterophoria Esophoria Alternating hyperphoria Exophoria 378.5 Paralytic strabismus Strabismus due to palsy: Total (external) ophthalmoplegia Third or oculomotor nerve Fourth or trochlear nerve Sixth or abducent nerve 378.6 Mechanical strabismus Brown's sheath syndrome Traumatic limitation of duction of Strabismus due to adhesions eye muscle 378.7 Other strabismus Duane's syndrome Progressive external ophthalmoplegia 378.8 Other disorders of binocular eye movements Conjugate gaze palsy or spasm Dissociated deviation of eye movements Convergence: Internuclear ophthalmoplegia excess insufficiency 378.9 Unspecified Ophthalmoplegia NOS Strabismus NOS 379 Other disorders of eye 379.0 Scleritis and episcleritis Episcleritis: Scleromalacia perforans NOS Sclerotenonitis ICD-9/Ch06.TXT - pg. 33 379.1 Other disorders of sclera Equatorial staphyloma Scleral ectasia 379.2 Disorders of vitreous body Asteroid hyalitis Vitreous: Synchysis scintillans detachment floaters hemorrhage opacities prolapse 379.3 Aphakia and other disorders of lens Dislocation of lens Subluxation of lens 379.4 Anomalies of pupillary function Adie pupil Miosis (persistent), not due to Anisocaria mydriattics Argyll Robertson phenomenon Pupillary reaction: or pupil (syphilitic) abnormal atypical(nonsyphilitic) tonic Hippus unequal 379.5 Nystagmus and other irregular eye movements Nystagmus: Nystagmus: NOS dissociated congenital latent deprivation 379.8 Other disorders of eye and adnexa 379.9 Unspecified DISEASES OF THE EAR AND MASTOID PROCESS (380-389) 380 Disorders of external ear 380.0 Perichondritis of pinna Perichondritis of auricle 380.1 Infective otitis externa Otitis externa: Swimmer's ear NOS diffuse hemorrhagica malignant ICD-9/Ch06.TXT - pg. 34 380.2 Other otitis externa Cholesteatoma of external ear (canal) Eczema or external ear (canal) Keratosis obturans 380.3 Noninfective disorders of pinna Acquired deformity: Hematoma: auricle auricle pinna pinna 380.4 Impacted cerumen Wax in ear 380.5 Acquired stenosis of external ear canal Collapse of external ear canal 380.8 Other disorders of external ear Exostosis of external ear canal 380.9 Unspecified 381 Nonsuppurative otitis media and Eustachian tube disorders 381.0 Acute nonsuppurative otitis media Acute tubotympanic catarrh Otitis media, acute: Otitis media, acute: secretory allergic seromucinous catarrhal serous exudative transudative mucoid with effusion 381.1 Chronic serous otitis media Chronic tubotympanal catarrh 381.2 Chronic mucoid otitis media Glue ear Otitis media, chronic mucinous Excludes: adhesive middle ear disease (385.1) 381.3 Other and unspecified chronic nonsuppurative otitis media Otitis media, chronic: Otitis media, chronic: allergic seromucinous exudative transudative secretory with effusion ICD-9/Ch06.TXT - pg. 35 381.4 Nonsuppurative otitis media, not specified as acute or chronic Otitis media: Otitis media: allergic seromucinous catarrhal serous exudative transudative mucoid with effusion secretory 381.5 Eustachian salpingitis 381.6 Obstruction of Eustachian tube Compression of Eustachian tube Stricture of Eustachian tube Stenosis of Eustachian tube 381.7 Patulous Eustachian tube 381.8 Other disorders of Eustachian tube 381.9 Unspecified Eustachian tube disorder 382 Suppurative and unspecified otitis media 382.0 Acute suppurative otitis media Otitis media, acute necrotizing (in): NOS Otitis media, acute purulent 382.1 Chronic tubotympanic suppurative otitis media Benign chronic suppurative otitis media Chronic tubotympanic disease 382.2 Chronic atticoantral suppurative otitis media Chronic atticoantral disease 382.3 Unspecified chronic suppurative otitis media Chronic purulent otitis media 382.4 Unspecified suppurative otitis media Purulent otitis media NOS 382.9 Unspecified otitis media Otitis media: NOS acute NOS chronic NOS ICD-9/Ch06.TXT - pg. 36 383 Mastoiditis and related conditions 383.0 Acute mastoiditis Abscess of mastoid Empyema of mastoid 383.1 Chronic mastoiditis Caries of mastoid Fistula of mastoid 383.2 Petrositis Inflammation of petrous bone (acute) (chronic) 383.3 Complications following mastoidectomy [Not to be used for underlying cause of death] Cyst } Granulations } of postmastoidectomy cavity Inflammation } 383.8 Other 383.9 Unspecified mastoiditis 384 Other disorders of tympanic membrane 384.0 Acute myringitis without mention of otitis media Acute tympanitis Bullous myringitis 384.1 Chronic myringitis without mention of otitis media Chronic tympanitis 384.2 Perforation of tympanic membrane Perforation of ear drum: NOS persistent post-traumatic postinflammatory 384.8 Other 384.9 Unspecified 385 Other disorders of middle ear and mastoid 385.0 Tympanosclerosis 385.1 Adhesive middle ear disease ICD-9/Ch06.TXT - pg. 37 Adhesive otitis Excludes: glue ear (381.2) 385.2 Other acquired abnormality of ear ossicles Ankylosis } Impaired mobility } of ear ossicles Partial loss } 385.3 Cholesteatoma of middle ear and mastoid Polyp of (middle) ear 385.8 Other 385.9 Unspecified 386 Vertiginous syndromes and other disorders of vestibular system Excludes: vertigo NOS (780.4) 386.0 M‚niŠre's disease Endolymphatic hydrops Lermoyez's syndrome M‚niŠre's syndrome or vertigo 386.1 Other and unspecified peripheral vertigo Aural vertigo Benign paroxysmal vertigo or nystagmus Otogenic vertigo Vestibular neuronitis 386.2 Vertigo of central origin Central positional nystagmus 386.3 Labyrinthitis 386.4 Labyrinthine fistula 386.5 Labyrinthine dysfunction Hypofunction } Hypersensitivity } of labyrinth Loss of function } 386.8 Other disorders of labyrinth 386.9 Unspecified vertiginous syndromes and labyrinthine disorders ICD-9/Ch06.TXT - pg. 38 387 Otosclerosis Includes: otospongiosis 387.0 Otosclerosis involving oval window, nonobliterative 387.1 Otosclerosis involving oval window, obliterative 387.2 Cochlear otosclerosis Otosclerosis involving: otic capsule round window 387.8 Other 387.9 Unspecified 388 Other disorders of ear 388.0 Degenerative and vascular disorders of ear Presbyacusis Transient ischemic deafness 388.1 Noise effects on inner ear Acoustic trauma (explosive) to ear Noise-induced hearing loss 388.2 Sudden hearing loss, unspecified 388.3 Tinnitus 388.4 Other abnormal auditory perception Auditory recruitment Hyperacusis Diplacusis Impairment of auditory discrimination 388.5 Disorders of acoustic nerve Acoustic neuritis: Degeneration of acoustic or eighth nerve NOS Disorder of acoustic or eighth nerve 388.6 Otorrhea Discharging ear 388.7 Otalgia Earache 388.8 Other ICD-9/Ch06.TXT - pg. 39 388.9 Unspecified 389 Deafness 389.0 Conductive deafness Conductive hearing loss 389.1 Sensorineural deafness Deafness: Hearing loss: central central neural neural perceptive perceptive sensory sensorineural sensory Excludes: abnormal auditory perception (388.4) psychogenic deafness (306.7) 389.2 Mixed conductive and sensorineural deafness Deafness or hearing loss of type in 389.0 with type in 389.1 389.7 Deaf mutism, not elsewhere classifiable 389.8 Other specified forms of deafness 389.9 Unspecified deafness Hearing loss NOS ICD-9/Ch06.TXT - pg. 40 VII. DISEASES OF THE CIRCULATORY SYSTEM ACUTE RHEUMATIC FEVER (390-392) 390 Rheumatic fever without mention of heart involvement Arthritis, rheumatic, acute or subacute Rheumatic fever (active) (acute) Rheumatism, articular, acute or subacute 391 Rheumatic fever with heart involvement Excludes: chronic heart diseases of rheumatic origin (393-398) unless rheumatic fever is also present or there is evidence of recrudescence or activity of the rheumatic process. 391.0 Acute rheumatic pericarditis Rheumatic pericarditis (acute) Any condition in 390 with pericarditis Excludes: when not specified as rheumatic (420.-) 391.1 Acute rheumatic endocarditis Rheumatic: endocarditis, acute valvulitis acute Any condition in 390 with endocarditis or valvulitis 391.2 Acute rheumatic myocarditis Any condition in 390 with myocarditis 391.8 Other acute rheumatic heart disease Rheumatic pancarditis, acute Any condition in 390 with other or multiple types of heart involvement 391.9 Acute rheumatic heart disease, unspecified Rheumatic: carditis, acute heart disease, active or acute Any condition in 390 with unspecified type of heart involvement 392 Rheumatic chorea Includes: Sydenham's chorea Excludes: Chorea: NOS (333.5) Huntington's (333.4) ICD-9/Ch07.TXT - pg. 1 392.0 With heart involvement Rheumatic chorea with heart involvement of any type classifiable under 391.- 392.9 Without mention of heart involvement CHRONIC RHEUMATIC HEART DISEASE (393-398) 393 Chronic rheumatic pericarditis Adherent pericardium, rheumatic Chronic rheumatic: mediastinopericarditis myopericarditis Excludes: when not specified as rheumatic (423.9) 394 Diseases of mitral valve 394.0 Mitral stenosis Mitral (valve) obstruction (rheumatic) 394.1 Rheumatic mitral insufficiency Rheumatic mitral: Rheumatic mitral: incompetence regurgitation Excludes: when not specified as rheumatic (424.0) 394.2 Mitral stenosis with insufficiency Mitral stenosis with incompetence or regurgitation 394.9 Other and unspecified Mitral (valve): Mitral (valve): disease (chronic) failure 395 Diseases of aortic valve Excludes: when not specified as rheumatic (424.1) 395.0 Rheumatic aortic stenosis Rheumatic aortic (valve) obstruction 395.1 Rheumatic aortic insufficiency Rheumatic aortic: incompetence regurgitation ICD-9/Ch07.TXT - pg. 2 395.2 Rheumatic aortic stenosis with insufficiency Rheumatic aortic stenosis with incompetence or regurgitation 395.9 Other and unspecified Rheumatic aortic (valve) disease 396 Diseases of mitral and aortic valves Involvement of both mitral and aortic valves whether specified as rheumatic or not 397 Diseases of other endocardial structures 397.0 Diseases of tricuspid valve Tricuspid (valve) (rheumatic): disease obstruction stenosis 397.1 Rheumatic diseases of pulmonary valve Excludes: when not specified as rheumatic (424.3) 397.9 Rheumatic diseases of endocardium, valve unspecified Rheumatic: endocarditis (chronic) valvulitis (chronic) Excludes: when not specified as rheumatic (424.9) 398 Other rheumatic heart disease 398.0 Rheumatic myocarditis Excludes: myocarditis not specified as rheumatic (429.0) 398.9 Other and unspecified Rheumatic: carditis heart disease NOS Excludes: carditis not specified as rheumatic (429.8) heart disease NOS not specified as rheumatic (429.9) ICD-9/Ch07.TXT - pg. 3